Abstract

The number of adults surviving with complex congenital heart diseases has increased dramatically over the past few years because of significant advances in diagnosis and medical and surgical care. Dilatation of the extramural coronary artery in cyanotic congenital heart disease is found in response to vascular remodeling induced by endothelial vasodilator substances like nitric oxide and vascular endothelial growth factor. Here, we describe a case of a 20 years young man who was diagnosed with congenitally corrected transposition of great vessels and underwent a successful bidirectional Glenn procedure. Pre-operative workup revealed hugely dilated, non-aneurysmal coronary arteries which were confirmed intra-operatively.