Abstract

The surgical and anaesthetics management of patients with giant umbilical hernia associated with Hurler’s Syndrome is a challenge because of many medical problems including progressive developmental delay, the observation that we report proves that the umbilical hernia that accompanies the Hurler’s syndrome may reach impressive size with a risk of complication; Spinal anaesthesia is contraindicated because of spinal anomalies. Laryngoscopy and fibreoptic bronchoscopy may be used for intubation in difficult cases the laryngeal mask airway has proved to be a useful additional aid Despite the risk, it may be wise to perform elective hernia repair using a prosthetic mesh in selected cases of Hurler’s syndrome.

Author(s): Smain Ait Yahia, Chouaib Sayah, Zineddine Soualili  

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