Moyamoya Disease

Moyamoya Disease is a rare, progressive cerebrovascular disorder caused by blocked arteries at the base of the brain in an area called the basal ganglia. The name “moyamoya” means “puff of smoke” in Japanese and describes the look of the tangle of tiny vessels formed to compensate for the blockage.

There are several types of revascularization surgery that can restore blood flow to the brain by opening narrowed blood vessels or by bypassing blocked arteries. Children usually respond better to revascularization surgery than adults, but the majority of individuals have no further strokes or related problems after surgery. Without surgery, the majority of individuals with Moyamoya disease will experience mental decline and multiple strokes because of the progressive narrowing of arteries. Without treatment, Moyamoya disease can be fatal as the result of intracerebral hemorrhage. Bypassing the occlusive segments is the aim of most surgical therapy.

In adults external carotid artery to middle cerebral artery (ECA-MCA) anastomoses can be performed as the vessels are larger. One of the surgical option is superficial temporal artery to middle cerebral artery (STA-MCA) bypass. Encephaloduroarteriosynangiosis is the treatment of choice in paediatric patients as their vessels are too small to allow direct anastomosis

Related Journals of Moyamoya Diseas
Medical & Surgical Urology, Surgery: Current Research, Tropical Medicine & Surgery, Archives of Surgical Oncology, Journal of Medical & Surgical Pathology, Journal of Vascular Medicine & Surgery, JAVA - Journal of the Association for Vascular Access, Journal of Vascular Investigation, Thoracic and Cardiovascular Surgeon, Vascular Disease Prevention.

 

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