Figure 1. In FAP the pancreas may be affected by ampullary and periampullary neoplasms, pancreatitis, pancreatic adenocarcinoma and a variety of rarer neoplasms. [From: Arthur William Mayo Robson, Percy John Cammidge. The Pancreas, Its Surgery and Pathology. Philadelphia, PA, USA: Saunders, 1907, p. 35.]